A case of relapsing panniculitis weberchristian disease has been extensively studied for approximately 21 months, from the inception of the disease until the death of the patient. Weberchristian disease radiology reference article. In this paper is outlined the course of the illness with the various studies conducted in an effort to ascertain the. Nodular nonsuppurative panniculitis describes a rare group of skin disorders characterized by tender, painful bumps below the surface of the skin subcutaneous nodules that usually lead to inflammation of the subcutaneous layer of fat panniculitis. Ever ready for a fight, weber carried a riding crop with him, a. Weberchristian disease, is a cutaneous condition characterized by recurrent subcutaneous nodules that heal with depression of the overlying skin it is a type of panniculitis. Christian weber ingenieur institut pasteur international. The topic weberchristian disease you are seeking is a synonym, or alternative name, or is closely related to the medical condition idiopathic lobular panniculitis. The patient suffered from rheumatoid arthritis for several years, but then developed relapsing. Weber christian disease is an uncommon inflammatory disease of the fatty tissues of the body.
Weberchristian disease is also referred to as idiopathic lobular panniculitis ilp and relapsing febrile nodular panniculitis syndrome the term weberchristian often refers to a. The differential diagnosis of a cardiac mass with features similar to csh includes genetic storage disorders, adult rhabdomyoma, weber christian disease, langerhans cell histiocytosis, rosaidorfman disease, erdheimchester disease, or cardiac inflammatory myofibroblastic tumor. Christian weber 25 august 1883 in polsingen 11 may 1945 in the swabian jura was a german nazi party nsdap official and member of the schutzstaffel ss biography. Weberchristian disease is an eponym for a form of panniculitis, idiopathic nodular panniculitis, which is characterized by subcutaneous nodules, inflammatory cells in the fat lobules, and systemic symptoms. June 5, 1826 in london, england was a german composer. Article in italian marra n, abrami f, chiavacci g, appicciafuoco a. Oct 07, 2019 weber christian disease is rare in adults and even rarer in children. Weberchristian disease or relapsing nodular panniculitis. Weberchristian disease or pfeiferweberchristian disease or idiopathic relapsing febrile nodular nonsuppurative panniculitis was initially defined as a rare inflammatory disorder of unknown etiology affecting subcutaneous adipose tissue inter alia 1 however, the understanding of lobular panniculitis has expanded and cases that were once diagnosed in the water basket of weber.
Weber christian disease is also referred to as idiopathic lobular panniculitis ilp and relapsing febrile nodular panniculitis syndrome. Get a printable copy pdf file of the complete article 2. Pfeiferweberchristian disease pwcd is a rare inflammatory disorder of the subcutaneous fatty tissue. Weberchristian disease is rare in adults and even rarer in children. Weberchristian disease, is a cutaneous condition characterized by recurrent subcutaneous nodules that heal with depression of the overlying skin. These nodules tend to be 12 centimeters in length and most often affect the legs and feet. Nodular nonsuppurative panniculitis genetic and rare. He was also an innovative composer for the clarinet, for which he wrote many works. Christian weber, residant valcourt 52, nous a quittes. En semiologie neurologique, cest lun des syndromes alternes. The term weber christian often refers to a group of diseases that involve the deep fat. Weberchristian disease definition of weberchristian. Full text full text is available as a scanned copy of the original print version. Panniculitis refers to a broad spectrum of diseases that involve inflammation of the subcutaneous fat layer of the skin.
Idiopathic lobular panniculitis is a condition in which inflammation occurs in the subcutaneous tissue, just beneath the skin. Clinical findings crops of subcutaneous nodules on the thighs, abdomen, arms and breasts, accompanied by fever, local inflammation, rheumatic complaints arthritis, arthralgia, myalgia, hepatosplenomegaly, abdominal pain and episcleritis. Oct 07, 2019 panniculitis refers to a broad spectrum of diseases that involve inflammation of the subcutaneous fat layer of the skin. Louisville ky dermatologist doctors weberchristian disease. Weber christian disease is an eponym for a form of panniculitis, idiopathic nodular panniculitis, which is characterized by subcutaneous nodules, inflammatory cells in the fat lobules, and systemic symptoms. A patient with pfeiferweberchristian disease successful.
Louisville kentucky dermatologist doctors physician directory weberchristian disease is also known as idiopathic lobular panniculitis. Weberchristian disease is an uncommon inflammatory disease of the fatty tissues of the body. Christian weber tabellarische angaben zu lebenslauf, forschungsinteressen, lehrerfahrungen univ. Biography edit along with the likes of emil maurice, ulrich graf, and max amann, weber, a bouncer at a bar, was amongst the earliest political associates of adolf hitler. Nach teilnahme am ersten weltkrieg im kaiserlichen heer zuletzt sergeant bzw. Christian weber 25 august 1883 in polsingen 11 may 1945 in the swabian jura was a german nazi party nsdap official and member of the schutzstaffel ss. Weber christian disease or pfeifer weber christian disease or idiopathic relapsing febrile nodular nonsuppurative panniculitis was initially defined as a rare inflammatory disorder of unknown etiology affecting subcutaneous adipose tissue inter alia 1. Weber christian disease is a skin disease characterized by relapsing fever and panniculitis. The differential diagnosis of a cardiac mass with features similar to csh includes genetic storage disorders, adult rhabdomyoma, weberchristian disease, langerhans cell histiocytosis, rosaidorfman disease, erdheimchester disease, or cardiac inflammatory myofibroblastic tumor.
The topic weber christian disease you are seeking is a synonym, or alternative name, or is closely related to the medical condition idiopathic lobular panniculitis. Christian weber facharzt fmh fur allgemeinmedizin manualmedizin, psychosomatische medizin, psychotherapie, medizinische hypnose. Learn about causes, risk factors, symptoms, diagnosis and treatment of this uncommon syndrome. It is named for frederick parkes weber and henry christian. Weberchristian syndrome a rare idiopathic condition that primarily affects adult females. It is a recurring inflammation of fatty layers of tissue present beneath the skin. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Rendezlui hommage en deposant des condoleances, des bougies ou encore des photos sur son espace souvenirs sur le site dans nos c. The diagnosis and therapy of this rare type of panniculitis is still controversial and will be discussed in this article. Webers work, especially his operas, greatly influenced the development of the romantic opera in german music.